Test Code PIPU Pipecolic Acid, Random, Urine
Performing Laboratory
Mayo Clinic Laboratories in RochesterSpecimen Type
UrineNecessary Information
Patient's age is required.
Specimen Required
Supplies: Urine tubes, 10 mL (T068)
Container/Tube: Plastic, 10-mL urine tube
Specimen Volume: 5 mL
Collection Instructions:
1. Collect a random urine specimen.
2. No preservative.
Specimen Minimum Volume
2 mL
Specimen Stability Information
Specimen Type | Temperature | Time | Special Container |
---|---|---|---|
Urine | Frozen (preferred) | 94 days | |
Refrigerated | 14 days |
Reference Values
≤31 days: ≤223.8 nmol/mg creatinine
32 days-5 months: ≤123.1 nmol/mg creatinine
6 months-11 months: ≤45.0 nmol/mg creatinine
≥1 year: ≤5.7 nmol/mg creatinine
Day(s) Performed
Tuesday
CPT Code Information
82542
Genetics Test Information
Pipecolic acid is not detected by conventional organic acid analysis of urine.
In the newborn period, pipecolic acid levels are more likely to be abnormal in urine than in plasma or serum. Abnormal levels of pipecolic acid should be interpreted together with the results of other biochemical markers of peroxisomal disorders, such as plasma C22-C26 very long-chain fatty acids, phytanic acid, pristanic acid, red blood cell plasmalogens, and bile acid intermediates.